Primary immunodeficienciesin adults



Cite item

Full Text

Open Access Open Access
Restricted Access Access granted
Restricted Access Subscription or Fee Access

Abstract

This article presents data on the prevalence of primary immunodeficiency diseases (PID ) in R ussia, reflects
the problems of the adult age patients with PID diagnosis. I t substantiates the necessity of inclusion of this
disease into the list of orphan diseases, that entitles the patients to be provided with expensive treatment irrespective
of the age and disability group. T he article shows clinical and laboratory criteria required for the general
practice doctors to diagnose timely the PID .

About the authors

T V Latysheva

N Kh Setdikova

Email: nsetdikova@mail.ru

E A Latysheva

A V Dmitrieva

A A Yurenkova

T V Latysheva

Institute of Immunology

Institute of Immunology

N Сh Setdikova

Institute of Immunology

Institute of Immunology

Е А Latysheva

Institute of Immunology

Institute of Immunology

A V Dmitrieva

Institute of Immunology

Institute of Immunology

A A Urenkova

Institute of Immunology

Institute of Immunology

References

  1. Аллергология и иммунология. Национальное руководство. Редакторы: P.M. Хаитов, Н.И. Ильина. «ГЭОТАР-медиа». М., 2009, с. 291-383.
  2. Резник И.Б. Современное состояние вопроса первичного иммунодефицита. Педиатрия. 1996, № 2, с. 4-14.
  3. Ten R.M. Primary immunodeficiencies. Mayo Clin. Proc. 1998, v. 73, p. 865-872.
  4. Ballow M. Primary immunodeficiency disorders: antibody deficiency. J. Allergy Clin. Immunol. 2002, v. 109, p. 581-591.
  5. Sorensen R.U., Moore С. Antibody deficiency syndromes. Pediatr. Clin. North Am. 2000, v. 47, p. 1225-1252.
  6. Сетдикова Н.Х. Диагностика и лечение врожденных иммунодефицитов у взрослых. Леч. врач. 2006, № 6, с. 44-48.
  7. XIVth meeting of the European Society for Immunodeficiencies in Istanbul, 2010.
  8. Ярцев М.Н., Яковлева К.П. Регистр первичных иммунодефицитных состояний Института иммунологии МЗ РФ. Физиол. и патол. иммунной системы. 2004, т. 8, № 2, с. 11-19.
  9. Кондратенко И.В., Сидоренко И.В. и соавт. Регистр первичных иммунодефицитов. Детская больница. 2002, № 24, с. 18-23.
  10. Медицинские стандарты, протоколы диагностики и лечения больных с аллергическими заболеваниями и нарушениями иммунной системы. М., «Медицина». 2000, с. 117.
  11. Conley M.E., Notarangelo L.D., Etzioni A. Diagnostic criteria for primary immunodeficiencies. Representing PAGID (Pan-American Group for Immunodeficiency) and ESID (European Society for Immunodeficiencies). Clin. Immunol. 1999, v. 93, p. 190-197.
  12. Buckley R.H. Primary immunodeficiency or not? Making the correct diagnosis. J. Allergy Clin. Immunol. 2006, 117 (4), p. 756-758.
  13. The 10 warning signs of primary immunodeficiency. The Jeffrey Modell Foundation, Copyright 2003. Accessed October 6, 2003, at:<http://npi.jmfworld.org/patienttopatient/index>. cfm section=warning signs.
  14. Wen L., Atkinson J.P., Giclas P.C. Clinical and laboratory evaluation of complement deficiency. J. Allergy Clin. Immunol. 2004, v. 113, p. 585-593.
  15. Bygum A., Fagerberg C.R., Ponard D., Monnier N. et al. Mutational spectrum and phenotypes in Danish families with hereditary angioedema because of C1 inhibitor deficiency. Allergy. 2011, v. 66, p. 76-84.
  16. Roche O., Blanch A., Duponchel С. et al. Hereditary Angioedema: The Mutation Spectrum of SERPING1/C1NH in a Large Spanish Cohort. HUMAN MUTATION. 2005, v. 26 (2), p. 135-144.
  17. World Immunology Conference «A global get together». New York, 1-5 June, 2011.
  18. Orange J.S., Grossman W.J., Navickis R.J., Wilkes M.M. Impact of trough IgG on pneumonia incidence in primary immunodeficiency: A meta-analysis of clinical studies. Clin. Immunol. 2010, v. 137 (1), p. 21-30.

Supplementary files

Supplementary Files
Action
1. JATS XML

Copyright © Pharmarus Print Media, 1970



This website uses cookies

You consent to our cookies if you continue to use our website.

About Cookies